{"id":7891,"date":"2018-05-27T16:44:24","date_gmt":"2018-05-27T19:44:24","guid":{"rendered":"https:\/\/blog.mindthegraph.com\/?p=7891"},"modified":"2022-10-18T14:37:51","modified_gmt":"2022-10-18T17:37:51","slug":"cystic-fibrosis","status":"publish","type":"post","link":"https:\/\/mindthegraph.com\/blog\/tr\/kistik-fibrozis\/","title":{"rendered":"Kistik fibrozis fark\u0131ndal\u0131k ay\u0131"},"content":{"rendered":"<p>May\u0131s ay\u0131 kistik fibrozis fark\u0131ndal\u0131k ay\u0131d\u0131r. Kistik fibrozis (KF) otozomal resesif ge\u00e7i\u015fli genetik bir hastal\u0131kt\u0131r. KF, kistik fibroz transmembran iletkenlik reg\u00fclat\u00f6r\u00fc (CFTR) kanal\u0131n\u0131 kodlayan gendeki mutasyonlardan kaynaklan\u0131r.  Bu protein, h\u00fccre zarlar\u0131 boyunca iyon ta\u015f\u0131nmas\u0131ndaki bir \u00e7e\u015fitlilikten sorumludur.<\/p>\n\n\n\n<p>Genetik ev referanslar\u0131na g\u00f6re <sup>1<\/sup>CFTR geni, kistik fibroz transmembran iletkenlik d\u00fczenleyicisi ad\u0131 verilen bir protein yapmak i\u00e7in talimatlar sa\u011flar:<\/p>\n\n\n\n<p>Bu protein mukus, ter, t\u00fck\u00fcr\u00fck, g\u00f6zya\u015f\u0131 ve sindirim enzimleri \u00fcreten h\u00fccrelerin zar\u0131nda bir kanal olarak i\u015flev g\u00f6r\u00fcr. Kanal, klor\u00fcr iyonlar\u0131 ad\u0131 verilen negatif y\u00fckl\u00fc par\u00e7ac\u0131klar\u0131 h\u00fccrelerin i\u00e7ine ve d\u0131\u015f\u0131na ta\u015f\u0131r. Klor\u00fcr iyonlar\u0131n\u0131n ta\u015f\u0131nmas\u0131, ince, serbest\u00e7e akan mukus \u00fcretimi i\u00e7in gerekli olan dokulardaki suyun hareketini kontrol etmeye yard\u0131mc\u0131 olur. Mukus, solunum yollar\u0131, sindirim sistemi, \u00fcreme sistemi ve di\u011fer organ ve dokular\u0131n i\u00e7 y\u00fczeyini ya\u011flayan ve koruyan kaygan bir maddedir.<\/p>\n\n\n\n<p><span style=\"font-weight: 400;\">CFTR proteini, sodyum iyonlar\u0131 ad\u0131 verilen pozitif y\u00fckl\u00fc par\u00e7ac\u0131klar\u0131 h\u00fccre zarlar\u0131 boyunca ta\u015f\u0131yan kanallar gibi di\u011fer kanallar\u0131n i\u015flevini de d\u00fczenler. Bu kanallar akci\u011ferler ve pankreas gibi organlar\u0131n normal i\u015flevi i\u00e7in gereklidir.<\/span><\/p>\n\n\n<div class=\"wp-block-image\">\n<figure class=\"aligncenter\"><a href=\"https:\/\/mindthegraph.com\/science_figures\" target=\"_blank\" rel=\"https:\/\/mindthegraph.com\/science_figures noopener\"><img decoding=\"async\" loading=\"lazy\" width=\"424\" height=\"306\" src=\"https:\/\/blog.mindthegraph.com\/wp-content\/uploads\/2018\/05\/dfaefqawefafc.png\" alt=\"dfaefqawefafc\" class=\"wp-image-7917\" srcset=\"https:\/\/mindthegraph.com\/blog\/wp-content\/uploads\/2018\/05\/dfaefqawefafc.png 424w, https:\/\/mindthegraph.com\/blog\/wp-content\/uploads\/2018\/05\/dfaefqawefafc-300x217.png 300w\" sizes=\"(max-width: 424px) 100vw, 424px\" \/><\/a><\/figure><\/div>\n\n\n<p>Bu durum ekzokrin bezlerinin i\u015fleyi\u015fini etkileyerek daha kal\u0131n, uzakla\u015ft\u0131r\u0131lmas\u0131 zor maddeler (mukus, ter veya pankreas enzimleri) \u00fcretir.<br>Bu nedenle kistik fibroz sindirim ve solunum sistemlerini ve ter bezlerini etkiler.<\/p>\n\n\n\n<p>Ancak hastal\u0131ktan en \u00e7ok solunum sistemi etkilenir. Akci\u011fer, hava yollar\u0131nda s\u0131k\u0131\u015f\u0131p kalabilen kal\u0131n mukus \u00fcretir. Kistik fibrozisli hastalarda kronik bakteriyel akci\u011fer enfeksiyonlar\u0131 ve sonunda son evre akci\u011fer hastal\u0131\u011f\u0131na neden olabilecek iltihaplanma geli\u015febilir.<br>Di\u011fer semptomlar salg\u0131l\u0131 \u00f6ks\u00fcr\u00fck, tekrarlayan zat\u00fcrre ve kronik bron\u015fittir.<\/p>\n\n\n\n<p>KF'li kad\u0131nlar hamile kalmakta daha fazla zorluk \u00e7ekerler \u00e7\u00fcnk\u00fc daha kal\u0131n servikal mukus spermin ge\u00e7mesini zorla\u015ft\u0131r\u0131r. Erkekler i\u00e7in bu daha da zordur. Erkeklerin yakla\u015f\u0131k 98%'si tamamen normal cinsel performans ve g\u00fcce sahip olmalar\u0131na ra\u011fmen k\u0131s\u0131rd\u0131r.<\/p>\n\n\n\n<p>Bug\u00fcn sizlerle payla\u015fmak \u00fczere CF'den 3 ba\u011flant\u0131 se\u00e7tim.<\/p>\n\n\n\n<div class=\"is-content-justification-center is-layout-flex wp-container-1 wp-block-buttons\">\n<div class=\"wp-block-button\"><a class=\"wp-block-button__link\" href=\"https:\/\/mindthegraph.com\/science_figures\">Dakikalar \u0130\u00e7inde Etkili Bilim Fig\u00fcrleri Olu\u015fturun<\/a><\/div>\n<\/div>\n\n\n\n<h3>Kistik fibrozisin gizemini \u00e7\u00f6zen iyi bir ileti\u015fim<\/h3>\n\n\n\n<center>\n<p><\/p><\/center>\n\n\n<p><iframe loading=\"lazy\" title=\"Kistik Fibrozis Nedir?\" width=\"800\" height=\"450\" src=\"https:\/\/www.youtube.com\/embed\/k4U5wyPzxJE?feature=oembed\" frameborder=\"0\" allow=\"accelerometer; autoplay; clipboard-write; encrypted-media; gyroscope; picture-in-picture\" allowfullscreen><\/iframe><\/p>\n\n\n\n<h3>Kistik Fibrozis ile Ya\u015fayan \u0130nsanlar\u0131n Bilmenizi \u0130stedi\u011fi 15 \u015eey - the buzzfeed list<\/h3>\n\n\n\n<p>KF ile ya\u015famak kolay de\u011fildir, bu nedenle destek almak ve bu konuda konu\u015fmak \u00e7ok \u00f6nemlidir. \u015eu buzzfeed listesine bak\u0131n<sup>2<\/sup> Kistik fibrozisli insanlar\u0131n rutinleri hakk\u0131nda konu\u015fmalar\u0131n\u0131 g\u00f6rmek i\u00e7in.<\/p>\n\n\n\n<div class=\"is-content-justification-center is-layout-flex wp-container-2 wp-block-buttons\">\n<div class=\"wp-block-button\"><a class=\"wp-block-button__link\" href=\"https:\/\/mindthegraph.com\/science_figures\">Mind The Graph'i Hemen \u015eimdi \u00dccretsiz Kullanmaya Ba\u015flay\u0131n!<\/a><\/div>\n<\/div>\n\n\n\n<h3>&nbsp;Di\u015f macununda bulunan antibakteriyel bir bile\u015fik<sup>3<\/sup>triklosan, gelecekte kistik fibrozis (KF) tedavisinin bir par\u00e7as\u0131 olabilir<\/h3>\n\n\n<div class=\"wp-block-image size-full wp-image-7921\">\n<figure class=\"aligncenter\"><a href=\"https:\/\/mindthegraph.com\/science_figures\" target=\"_blank\" rel=\"https:\/\/mindthegraph.com\/science_figures noopener\"><img decoding=\"async\" loading=\"lazy\" width=\"800\" height=\"420\" src=\"https:\/\/blog.mindthegraph.com\/wp-content\/uploads\/2018\/05\/31846788804_1d47e5b32b_b_0-1.jpg\" alt=\"Bu g\u00f6r\u00fcnt\u00fc, milyonlarca tek h\u00fccreli bakteri Pseudomonas aeruginosa&#039;dan olu\u015fan karma\u015f\u0131k bir koloniyi g\u00f6stermektedir\" class=\"wp-image-7921\" srcset=\"https:\/\/mindthegraph.com\/blog\/wp-content\/uploads\/2018\/05\/31846788804_1d47e5b32b_b_0-1.jpg 800w, https:\/\/mindthegraph.com\/blog\/wp-content\/uploads\/2018\/05\/31846788804_1d47e5b32b_b_0-1-300x158.jpg 300w, https:\/\/mindthegraph.com\/blog\/wp-content\/uploads\/2018\/05\/31846788804_1d47e5b32b_b_0-1-768x403.jpg 768w\" sizes=\"(max-width: 800px) 100vw, 800px\" \/><\/a><figcaption>Bu g\u00f6r\u00fcnt\u00fc, milyonlarca tek h\u00fccreli bakteri Pseudomonas aeruginosa'dan olu\u015fan karma\u015f\u0131k bir koloniyi g\u00f6stermektedir<\/figcaption><\/figure><\/div>\n\n\n<p>Ara\u015ft\u0131rma&nbsp;<strong><em>Triklosan, Pseudomonas aeruginosa biyofilmlerinin eradikasyonu i\u00e7in bir aminoglikozid adjuvan\u0131d\u0131r <sup>4<\/sup>&nbsp;<\/em><\/strong>kombinasyonun P. aeruginosa biyofilmleri i\u00e7indeki h\u00fccrelerin hem \u00f6ld\u00fcr\u00fclme oran\u0131n\u0131 hem de derecesini art\u0131rd\u0131\u011f\u0131n\u0131 ve bunun KF hastalar\u0131nda biyofilm enfeksiyonlar\u0131n\u0131n tedavisi i\u00e7in \u00f6nemli klinik etkileri oldu\u011funu g\u00f6stermektedir.<\/p>\n\n\n\n<ol><li><a href=\"https:\/\/medlineplus.gov\/genetics\/gene\/cftr\/\" target=\"_blank\" rel=\"noreferrer noopener\">CFTR geni kistik fibroz transmembran iletkenlik d\u00fczenleyicisi.<\/a><\/li><li><a href=\"https:\/\/www.buzzfeed.com\/ailbhemalone\/living-with-cystic-fibrosis?utm_term=.srElmo7oO#.nyQVXbMb2\" target=\"_blank\" rel=\"noreferrer noopener\">Kistik Fibrozis ile Ya\u015fayan \u0130nsanlar\u0131n Bilmenizi \u0130stedi\u011fi 15 \u015eey.<\/a><\/li><li><a href=\"https:\/\/cysticfibrosisnewstoday.com\/2018\/05\/21\/cystic-fibrosis-antiobiotic-more-effective-in-combo-with-toothpaste-antibacterial-study-suggests\/\" target=\"_blank\" rel=\"noreferrer noopener\">Di\u015f Macunundaki Antibakteriyel Triklosan, \u00c7al\u0131\u015fma \u00d6nerilerine G\u00f6re Kombine Antibiyotik Tedavisi Olarak \u0130yi \u0130\u015fe Yar\u0131yor.<\/a><\/li><li><a href=\"https:\/\/journals.asm.org\/doi\/full\/10.1128\/AAC.00146-18\" target=\"_blank\" rel=\"noreferrer noopener\">Triklosan, Aminoglikozidlerin Eradikasyonu \u0130\u00e7in Bir Yard\u0131mc\u0131 Maddedir&nbsp;<em>Pseudomonas aeruginosa<\/em>&nbsp;Biyofilmler.<\/a><\/li><\/ol>","protected":false},"excerpt":{"rendered":"<p>May\u0131s ay\u0131 kistik fibrozis fark\u0131ndal\u0131k ay\u0131d\u0131r. Kistik fibrozis (KF) otozomal resesif ge\u00e7i\u015fli genetik bir hastal\u0131kt\u0131r. KF, kistik fibroz transmembran iletkenlik reg\u00fclat\u00f6r\u00fc (CFTR) kanal\u0131n\u0131 kodlayan gendeki mutasyonlardan kaynaklan\u0131r.  Bu protein, h\u00fccre zarlar\u0131 boyunca iyon ta\u015f\u0131nmas\u0131ndaki bir de\u011fi\u015fiklikten sorumludur. Genetics home referanslar\u0131na g\u00f6re 1, CFTR geni [...]<\/p>","protected":false},"author":11,"featured_media":7919,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"image","meta":[],"categories":[959,28],"tags":[554,250],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v19.9 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Cystic fibrosis awareness month - Mind the Graph Blog<\/title>\n<meta name=\"description\" content=\"May is the cystic fibrosis awareness month. Cystic fibrosis (CF) is an autosomal recessive genetic disorder. I chose 3 links of CF to share with you today:\" \/>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/mindthegraph.com\/blog\/tr\/kistik-fibrozis\/\" \/>\n<meta property=\"og:locale\" content=\"tr_TR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Cystic fibrosis awareness month - Mind the Graph Blog\" \/>\n<meta property=\"og:description\" content=\"May is the cystic fibrosis awareness month. Cystic fibrosis (CF) is an autosomal recessive genetic disorder. 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