{"id":7891,"date":"2018-05-27T16:44:24","date_gmt":"2018-05-27T19:44:24","guid":{"rendered":"https:\/\/blog.mindthegraph.com\/?p=7891"},"modified":"2022-10-18T14:37:51","modified_gmt":"2022-10-18T17:37:51","slug":"cystic-fibrosis","status":"publish","type":"post","link":"https:\/\/mindthegraph.com\/blog\/sl\/cisticna-fibroza\/","title":{"rendered":"Mesec ozave\u0161\u010danja o cisti\u010dni fibrozi"},"content":{"rendered":"<p>Maj je mesec ozave\u0161\u010danja o cisti\u010dni fibrozi. Cisti\u010dna fibroza (CF) je avtosomno recesivna genetska bolezen. CF je posledica mutacij v genu, ki kodira kanal regulatorja transmembranske prevodnosti cisti\u010dne fibroze (CFTR).  Ta beljakovina je odgovorna za spremembe pri prenosu ionov skozi celi\u010dne membrane.<\/p>\n\n\n\n<p>V skladu z referencami Genetics home <sup>1<\/sup>, gen CFTR zagotavlja navodila za izdelavo beljakovine, imenovane regulator transmembranske prevodnosti pri cisti\u010dni fibrozi:<\/p>\n\n\n\n<p>Ta beljakovina deluje kot kanal skozi membrano celic, ki proizvajajo sluz, znoj, slino, solze in prebavne encime. Kanal prena\u0161a negativno nabite delce, imenovane kloridni ioni, v celice in iz njih. Prenos kloridnih ionov pomaga nadzorovati gibanje vode v tkivih, kar je potrebno za proizvodnjo tanke, prosto teko\u010de sluzi. Sluz je spolzka snov, ki ma\u017ee in \u0161\u010diti sluznico dihalnih poti, prebavnega sistema, reproduktivnega sistema ter drugih organov in tkiv.<\/p>\n\n\n\n<p><span style=\"font-weight: 400;\">Beljakovina CFTR uravnava tudi delovanje drugih kanalov, na primer tistih, ki prena\u0161ajo pozitivno nabite delce, imenovane natrijevi ioni, skozi celi\u010dne membrane. Ti kanali so potrebni za normalno delovanje organov, kot so plju\u010da in trebu\u0161na slinavka.<\/span><\/p>\n\n\n<div class=\"wp-block-image\">\n<figure class=\"aligncenter\"><a href=\"https:\/\/mindthegraph.com\/science_figures\" target=\"_blank\" rel=\"https:\/\/mindthegraph.com\/science_figures noopener\"><img decoding=\"async\" loading=\"lazy\" width=\"424\" height=\"306\" src=\"https:\/\/blog.mindthegraph.com\/wp-content\/uploads\/2018\/05\/dfaefqawefafc.png\" alt=\"dfaefqawefafc\" class=\"wp-image-7917\" srcset=\"https:\/\/mindthegraph.com\/blog\/wp-content\/uploads\/2018\/05\/dfaefqawefafc.png 424w, https:\/\/mindthegraph.com\/blog\/wp-content\/uploads\/2018\/05\/dfaefqawefafc-300x217.png 300w\" sizes=\"(max-width: 424px) 100vw, 424px\" \/><\/a><\/figure><\/div>\n\n\n<p>To vpliva na delovanje eksokrinih \u017elez, ki proizvajajo gostej\u0161e, te\u017eko odstranljive snovi (sluz, znoj ali encime trebu\u0161ne slinavke).<br>Zato cisti\u010dna fibroza prizadene prebavni in dihalni sistem ter \u017eleze znojnice.<\/p>\n\n\n\n<p>Bolezen najbolj prizadene dihalni sistem. Plju\u010da proizvajajo gosto sluz, ki se lahko ujame v dihalnih poteh. Pri bolnikih s cisti\u010dno fibrozo se lahko razvijejo kroni\u010dne bakterijske plju\u010dne oku\u017ebe in vnetja, ki lahko s\u010dasoma povzro\u010dijo kon\u010dno fazo plju\u010dne bolezni.<br>Drugi simptomi so ka\u0161elj z izlo\u010danjem, ponavljajo\u010da se plju\u010dnica in kroni\u010dni bronhitis.<\/p>\n\n\n\n<p>\u017denske s CF te\u017eje zanosijo, ker gostej\u0161a sluz materni\u010dnega vratu ote\u017euje prehod spermijev. Pri mo\u0161kih je to \u0161e te\u017eje. Pribli\u017eno 98% mo\u0161kih je neplodnih, \u010deprav imajo povsem normalno spolno zmogljivost in potenco.<\/p>\n\n\n\n<p>Izbrala sem 3 povezave CF, ki jih bom danes delila z vami.<\/p>\n\n\n\n<div class=\"is-content-justification-center is-layout-flex wp-container-1 wp-block-buttons\">\n<div class=\"wp-block-button\"><a class=\"wp-block-button__link\" href=\"https:\/\/mindthegraph.com\/science_figures\">Ustvarjanje u\u010dinkovitih znanstvenih figur v nekaj minutah<\/a><\/div>\n<\/div>\n\n\n\n<h3>Dobro sporo\u010dilo, ki demistificira cisti\u010dno fibrozo<\/h3>\n\n\n\n<center>\n<p><\/p><\/center>\n\n\n<p><iframe loading=\"lazy\" title=\"Kaj je cisti\u010dna fibroza?\" width=\"800\" height=\"450\" src=\"https:\/\/www.youtube.com\/embed\/k4U5wyPzxJE?feature=oembed\" frameborder=\"0\" allow=\"accelerometer; autoplay; clipboard-write; encrypted-media; gyroscope; picture-in-picture\" allowfullscreen><\/iframe><\/p>\n\n\n\n<h3>15 stvari, ki bi jih radi vedeli od ljudi s cisti\u010dno fibrozo - seznam buzzfeed<\/h3>\n\n\n\n<p>\u017divljenje s CF ni lahko, zato je zelo pomembno, da imate podporo in se o tem pogovarjate. Oglejte si ta seznam buzzfeed<sup>2<\/sup> , da bi videli, kako ljudje s cisti\u010dno fibrozo govorijo o svoji rutini.<\/p>\n\n\n\n<div class=\"is-content-justification-center is-layout-flex wp-container-2 wp-block-buttons\">\n<div class=\"wp-block-button\"><a class=\"wp-block-button__link\" href=\"https:\/\/mindthegraph.com\/science_figures\">Za\u010dnite uporabljati Mind The Graph prav zdaj brezpla\u010dno!<\/a><\/div>\n<\/div>\n\n\n\n<h3>&nbsp;Antibakterijska spojina v zobni pasti<sup>3<\/sup>, imenovan triklosan, bo morda del prihodnjega zdravljenja cisti\u010dne fibroze (CF).<\/h3>\n\n\n<div class=\"wp-block-image size-full wp-image-7921\">\n<figure class=\"aligncenter\"><a href=\"https:\/\/mindthegraph.com\/science_figures\" target=\"_blank\" rel=\"https:\/\/mindthegraph.com\/science_figures noopener\"><img decoding=\"async\" loading=\"lazy\" width=\"800\" height=\"420\" src=\"https:\/\/blog.mindthegraph.com\/wp-content\/uploads\/2018\/05\/31846788804_1d47e5b32b_b_0-1.jpg\" alt=\"Slika prikazuje zapleteno kolonijo milijonov enoceli\u010dnih bakterij Pseudomonas aeruginosa.\" class=\"wp-image-7921\" srcset=\"https:\/\/mindthegraph.com\/blog\/wp-content\/uploads\/2018\/05\/31846788804_1d47e5b32b_b_0-1.jpg 800w, https:\/\/mindthegraph.com\/blog\/wp-content\/uploads\/2018\/05\/31846788804_1d47e5b32b_b_0-1-300x158.jpg 300w, https:\/\/mindthegraph.com\/blog\/wp-content\/uploads\/2018\/05\/31846788804_1d47e5b32b_b_0-1-768x403.jpg 768w\" sizes=\"(max-width: 800px) 100vw, 800px\" \/><\/a><figcaption>Slika prikazuje zapleteno kolonijo milijonov enoceli\u010dnih bakterij Pseudomonas aeruginosa.<\/figcaption><\/figure><\/div>\n\n\n<p>Raziskava&nbsp;<strong><em>Triklosan je aminoglikozidni adjuvans za eradikacijo biofilmov Pseudomonas aeruginosa <sup>4<\/sup>&nbsp;<\/em><\/strong>ka\u017eejo, da kombinacija pove\u010da hitrost in stopnjo uni\u010denja celic v biofilmih P. aeruginosa, kar ima pomembne klini\u010dne posledice za zdravljenje oku\u017eb z biofilmi pri bolnikih s CF.<\/p>\n\n\n\n<ol><li><a href=\"https:\/\/medlineplus.gov\/genetics\/gene\/cftr\/\" target=\"_blank\" rel=\"noreferrer noopener\">CFTR gen regulator transmembranske prevodnosti pri cisti\u010dni fibrozi.<\/a><\/li><li><a href=\"https:\/\/www.buzzfeed.com\/ailbhemalone\/living-with-cystic-fibrosis?utm_term=.srElmo7oO#.nyQVXbMb2\" target=\"_blank\" rel=\"noreferrer noopener\">15 stvari, ki jih \u017eelijo vedeti ljudje, ki \u017eivijo s cisti\u010dno fibrozo.<\/a><\/li><li><a href=\"https:\/\/cysticfibrosisnewstoday.com\/2018\/05\/21\/cystic-fibrosis-antiobiotic-more-effective-in-combo-with-toothpaste-antibacterial-study-suggests\/\" target=\"_blank\" rel=\"noreferrer noopener\">Triklosan, antibakterijsko sredstvo v zobni pasti, dobro deluje kot kombinirano antibioti\u010dno zdravljenje, ka\u017ee \u0161tudija.<\/a><\/li><li><a href=\"https:\/\/journals.asm.org\/doi\/full\/10.1128\/AAC.00146-18\" target=\"_blank\" rel=\"noreferrer noopener\">Triklosan je aminoglikozidni adjuvans za izkoreninjenje&nbsp;<em>Pseudomonas aeruginosa<\/em>&nbsp;Biofilmi.<\/a><\/li><\/ol>","protected":false},"excerpt":{"rendered":"<p>Maj je mesec ozave\u0161\u010danja o cisti\u010dni fibrozi. Cisti\u010dna fibroza (CF) je avtosomno recesivna genetska bolezen. CF je posledica mutacij v genu, ki kodira kanal regulatorja transmembranske prevodnosti cisti\u010dne fibroze (CFTR).  Ta beljakovina je odgovorna za spremembe pri prenosu ionov skozi celi\u010dne membrane. V skladu z doma\u010dimi referencami Genetics 1 gen CFTR zagotavlja [...]<\/p>","protected":false},"author":11,"featured_media":7919,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"image","meta":[],"categories":[959,28],"tags":[554,250],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v19.9 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Cystic fibrosis awareness month - Mind the Graph Blog<\/title>\n<meta name=\"description\" content=\"May is the cystic fibrosis awareness month. Cystic fibrosis (CF) is an autosomal recessive genetic disorder. I chose 3 links of CF to share with you today:\" \/>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/mindthegraph.com\/blog\/sl\/cisticna-fibroza\/\" \/>\n<meta property=\"og:locale\" content=\"sl_SI\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Cystic fibrosis awareness month - Mind the Graph Blog\" \/>\n<meta property=\"og:description\" content=\"May is the cystic fibrosis awareness month. Cystic fibrosis (CF) is an autosomal recessive genetic disorder. I chose 3 links of CF to share with you today:\" \/>\n<meta property=\"og:url\" content=\"https:\/\/mindthegraph.com\/blog\/sl\/cisticna-fibroza\/\" \/>\n<meta property=\"og:site_name\" content=\"Mind the Graph Blog\" \/>\n<meta property=\"article:published_time\" content=\"2018-05-27T19:44:24+00:00\" \/>\n<meta property=\"article:modified_time\" content=\"2022-10-18T17:37:51+00:00\" \/>\n<meta property=\"og:image\" content=\"https:\/\/mindthegraph.com\/blog\/wp-content\/uploads\/2018\/05\/31846788804_1d47e5b32b_b_0.jpg\" \/>\n\t<meta property=\"og:image:width\" content=\"800\" \/>\n\t<meta property=\"og:image:height\" content=\"420\" \/>\n\t<meta property=\"og:image:type\" content=\"image\/jpeg\" \/>\n<meta name=\"author\" content=\"Fabiola Soares\" \/>\n<meta name=\"twitter:card\" content=\"summary_large_image\" \/>\n<meta name=\"twitter:label1\" content=\"Written by\" \/>\n\t<meta name=\"twitter:data1\" content=\"Fabiola Soares\" \/>\n\t<meta name=\"twitter:label2\" content=\"Est. reading time\" \/>\n\t<meta name=\"twitter:data2\" content=\"3 minutes\" \/>\n<!-- \/ Yoast SEO plugin. -->","yoast_head_json":{"title":"Cystic fibrosis awareness month - Mind the Graph Blog","description":"May is the cystic fibrosis awareness month. 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