{"id":7891,"date":"2018-05-27T16:44:24","date_gmt":"2018-05-27T19:44:24","guid":{"rendered":"https:\/\/blog.mindthegraph.com\/?p=7891"},"modified":"2022-10-18T14:37:51","modified_gmt":"2022-10-18T17:37:51","slug":"cystic-fibrosis","status":"publish","type":"post","link":"https:\/\/mindthegraph.com\/blog\/ro\/fibroza-chistica\/","title":{"rendered":"Luna de con\u0219tientizare a fibrozei chistice"},"content":{"rendered":"<p>Luna mai este luna de con\u0219tientizare a fibrozei chistice. Fibroza chistic\u0103 (FC) este o boal\u0103 genetic\u0103 autosomal recesiv\u0103. Fibroza chistic\u0103 este cauzat\u0103 de muta\u021bii \u00een gena care codific\u0103 canalul de reglare a conductan\u021bei transmembranare a fibrozei chistice (CFTR).  Aceast\u0103 protein\u0103 este responsabil\u0103 de o varia\u021bie \u00een transportul ionilor prin membranele celulare.<\/p>\n\n\n\n<p>\u00cen conformitate cu Genetica referin\u021be la domiciliu <sup>1<\/sup>, gena CFTR furnizeaz\u0103 instruc\u021biuni pentru producerea unei proteine numite regulatorul de conductan\u021b\u0103 transmembranar\u0103 a fibrozei chistice:<\/p>\n\n\n\n<p>Aceast\u0103 protein\u0103 func\u021bioneaz\u0103 ca un canal prin membrana celulelor care produc mucus, transpira\u021bie, saliv\u0103, lacrimi \u0219i enzime digestive. Canalul transport\u0103 particule \u00eenc\u0103rcate negativ, numite ioni de clorur\u0103, \u00een interiorul \u0219i \u00een afara celulelor. Transportul ionilor de clorur\u0103 ajut\u0103 la controlul mi\u0219c\u0103rii apei \u00een \u021besuturi, ceea ce este necesar pentru producerea de mucus sub\u021bire \u0219i care curge liber. Mucusul este o substan\u021b\u0103 alunecoas\u0103 care lubrifiaz\u0103 \u0219i protejeaz\u0103 mucoasa c\u0103ilor respiratorii, a sistemului digestiv, a sistemului reproduc\u0103tor \u0219i a altor organe \u0219i \u021besuturi.<\/p>\n\n\n\n<p><span style=\"font-weight: 400;\">Proteina CFTR regleaz\u0103, de asemenea, func\u021bia altor canale, cum ar fi cele care transport\u0103 particule \u00eenc\u0103rcate pozitiv numite ioni de sodiu prin membranele celulare. Aceste canale sunt necesare pentru func\u021bionarea normal\u0103 a unor organe precum pl\u0103m\u00e2nii \u0219i pancreasul.<\/span><\/p>\n\n\n<div class=\"wp-block-image\">\n<figure class=\"aligncenter\"><a href=\"https:\/\/mindthegraph.com\/science_figures\" target=\"_blank\" rel=\"https:\/\/mindthegraph.com\/science_figures noopener\"><img decoding=\"async\" loading=\"lazy\" width=\"424\" height=\"306\" src=\"https:\/\/blog.mindthegraph.com\/wp-content\/uploads\/2018\/05\/dfaefqawefafc.png\" alt=\"dfaefqawefafc\" class=\"wp-image-7917\" srcset=\"https:\/\/mindthegraph.com\/blog\/wp-content\/uploads\/2018\/05\/dfaefqawefafc.png 424w, https:\/\/mindthegraph.com\/blog\/wp-content\/uploads\/2018\/05\/dfaefqawefafc-300x217.png 300w\" sizes=\"(max-width: 424px) 100vw, 424px\" \/><\/a><\/figure><\/div>\n\n\n<p>Aceasta afecteaz\u0103 func\u021bionarea glandelor exocrine, produc\u00e2nd substan\u021be mai groase \u0219i greu de eliminat (mucus, transpira\u021bie sau enzime pancreatice).<br>Din acest motiv, fibroza chistic\u0103 afecteaz\u0103 sistemele digestiv \u0219i respirator \u0219i glandele sudoripare.<\/p>\n\n\n\n<p>Cu toate acestea, sistemul respirator este cel mai afectat de boal\u0103. Pl\u0103m\u00e2nul produce un mucus gros care poate r\u0103m\u00e2ne blocat \u00een c\u0103ile respiratorii. Pacien\u021bii cu fibroz\u0103 chistic\u0103 pot dezvolta infec\u021bii pulmonare bacteriene cronice \u0219i inflama\u021bii care, \u00een cele din urm\u0103, pot provoca o boal\u0103 pulmonar\u0103 \u00een stadiu terminal.<br>Alte simptome sunt tusea cu secre\u021bii, pneumonia recurent\u0103 \u0219i bron\u0219ita cronic\u0103.<\/p>\n\n\n\n<p>Femeile cu fibroz\u0103 chistic\u0103 au mai multe dificult\u0103\u021bi \u00een a r\u0103m\u00e2ne \u00eens\u0103rcinate, deoarece mucusul cervical mai gros \u00eengreuneaz\u0103 trecerea spermatozoizilor. La b\u0103rba\u021bi este \u0219i mai dificil. Aproximativ 98% dintre b\u0103rba\u021bi sunt sterili, de\u0219i au performan\u021be \u0219i poten\u021b\u0103 sexual\u0103 absolut normale.<\/p>\n\n\n\n<p>Am ales 3 link-uri de CF pentru a le \u00eemp\u0103rt\u0103\u0219i cu voi ast\u0103zi.<\/p>\n\n\n\n<div class=\"is-content-justification-center is-layout-flex wp-container-1 wp-block-buttons\">\n<div class=\"wp-block-button\"><a class=\"wp-block-button__link\" href=\"https:\/\/mindthegraph.com\/science_figures\">Crea\u021bi figuri \u0219tiin\u021bifice eficiente \u00een c\u00e2teva minute<\/a><\/div>\n<\/div>\n\n\n\n<h3>O bun\u0103 comunicare care demistific\u0103 fibroza chistic\u0103<\/h3>\n\n\n\n<center>\n<p><\/p><\/center>\n\n\n<p><iframe loading=\"lazy\" title=\"Ce este fibroza chistic\u0103?\" width=\"800\" height=\"450\" src=\"https:\/\/www.youtube.com\/embed\/k4U5wyPzxJE?feature=oembed\" frameborder=\"0\" allow=\"accelerometer; autoplay; clipboard-write; encrypted-media; gyroscope; picture-in-picture\" allowfullscreen><\/iframe><\/p>\n\n\n\n<h3>15 lucruri pe care oamenii care tr\u0103iesc cu fibroz\u0103 chistic\u0103 vor s\u0103 le \u0219tii - the buzzfeed list<\/h3>\n\n\n\n<p>Nu este u\u0219or s\u0103 tr\u0103ie\u0219ti cu fibroza chistic\u0103, a\u0219a c\u0103 este foarte important s\u0103 ai sprijin \u0219i s\u0103 vorbe\u0219ti despre asta. Uita\u021bi-v\u0103 la aceast\u0103 list\u0103 Buzzfeed<sup>2<\/sup> , pentru a vedea persoane cu fibroz\u0103 chistic\u0103 vorbind despre rutina lor.<\/p>\n\n\n\n<div class=\"is-content-justification-center is-layout-flex wp-container-2 wp-block-buttons\">\n<div class=\"wp-block-button\"><a class=\"wp-block-button__link\" href=\"https:\/\/mindthegraph.com\/science_figures\">\u00cencepe\u021bi s\u0103 utiliza\u021bi Mind The Graph chiar acum, gratuit!<\/a><\/div>\n<\/div>\n\n\n\n<h3>&nbsp;Un compus antibacterian g\u0103sit \u00een pasta de din\u021bi<sup>3<\/sup>, numit triclosan, ar putea face parte dintr-un viitor tratament pentru fibroza chistic\u0103 (FC)<\/h3>\n\n\n<div class=\"wp-block-image size-full wp-image-7921\">\n<figure class=\"aligncenter\"><a href=\"https:\/\/mindthegraph.com\/science_figures\" target=\"_blank\" rel=\"https:\/\/mindthegraph.com\/science_figures noopener\"><img decoding=\"async\" loading=\"lazy\" width=\"800\" height=\"420\" src=\"https:\/\/blog.mindthegraph.com\/wp-content\/uploads\/2018\/05\/31846788804_1d47e5b32b_b_0-1.jpg\" alt=\"Aceast\u0103 imagine arat\u0103 o colonie complex\u0103 de milioane de milioane de bacterii unicelulare Pseudomonas aeruginosa.\" class=\"wp-image-7921\" srcset=\"https:\/\/mindthegraph.com\/blog\/wp-content\/uploads\/2018\/05\/31846788804_1d47e5b32b_b_0-1.jpg 800w, https:\/\/mindthegraph.com\/blog\/wp-content\/uploads\/2018\/05\/31846788804_1d47e5b32b_b_0-1-300x158.jpg 300w, https:\/\/mindthegraph.com\/blog\/wp-content\/uploads\/2018\/05\/31846788804_1d47e5b32b_b_0-1-768x403.jpg 768w\" sizes=\"(max-width: 800px) 100vw, 800px\" \/><\/a><figcaption>Aceast\u0103 imagine arat\u0103 o colonie complex\u0103 de milioane de milioane de bacterii unicelulare Pseudomonas aeruginosa.<\/figcaption><\/figure><\/div>\n\n\n<p>Cercetarea&nbsp;<strong><em>Triclosanul este un adjuvant aminoglicozidic pentru eradicarea biofilmelor de Pseudomonas aeruginosa <sup>4<\/sup>&nbsp;<\/em><\/strong>arat\u0103 c\u0103 aceast\u0103 combina\u021bie cre\u0219te at\u00e2t rata, c\u00e2t \u0219i gradul de distrugere a celulelor din biofilmele de P. aeruginosa, ceea ce are implica\u021bii clinice importante pentru tratamentul infec\u021biilor cu biofilme la pacien\u021bii cu FC.<\/p>\n\n\n\n<ol><li><a href=\"https:\/\/medlineplus.gov\/genetics\/gene\/cftr\/\" target=\"_blank\" rel=\"noreferrer noopener\">Gena CFTR - regulator de conductan\u021b\u0103 transmembranar\u0103 a fibrozei chistice.<\/a><\/li><li><a href=\"https:\/\/www.buzzfeed.com\/ailbhemalone\/living-with-cystic-fibrosis?utm_term=.srElmo7oO#.nyQVXbMb2\" target=\"_blank\" rel=\"noreferrer noopener\">15 lucruri pe care persoanele care tr\u0103iesc cu fibroz\u0103 chistic\u0103 vor s\u0103 le \u0219tii.<\/a><\/li><li><a href=\"https:\/\/cysticfibrosisnewstoday.com\/2018\/05\/21\/cystic-fibrosis-antiobiotic-more-effective-in-combo-with-toothpaste-antibacterial-study-suggests\/\" target=\"_blank\" rel=\"noreferrer noopener\">Triclosan, antibacterianul din pasta de din\u021bi, func\u021bioneaz\u0103 bine ca tratament combinat cu antibiotice, sugereaz\u0103 un studiu.<\/a><\/li><li><a href=\"https:\/\/journals.asm.org\/doi\/full\/10.1128\/AAC.00146-18\" target=\"_blank\" rel=\"noreferrer noopener\">Triclosanul este un adjuvant aminoglicozidic pentru eradicarea&nbsp;<em>Pseudomonas aeruginosa<\/em>&nbsp;Biofilme.<\/a><\/li><\/ol>","protected":false},"excerpt":{"rendered":"<p>Luna mai este luna de con\u0219tientizare a fibrozei chistice. Fibroza chistic\u0103 (FC) este o boal\u0103 genetic\u0103 autosomal recesiv\u0103. Fibroza chistic\u0103 este cauzat\u0103 de muta\u021bii \u00een gena care codific\u0103 canalul de reglare a conductan\u021bei transmembranare a fibrozei chistice (CFTR).  Aceast\u0103 protein\u0103 este responsabil\u0103 de o varia\u021bie \u00een transportul ionilor prin membranele celulare. Potrivit cu Genetics home referin\u021be 1, gena CFTR asigur\u0103 [...]<\/p>","protected":false},"author":11,"featured_media":7919,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"image","meta":[],"categories":[959,28],"tags":[554,250],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v19.9 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Cystic fibrosis awareness month - Mind the Graph Blog<\/title>\n<meta name=\"description\" content=\"May is the cystic fibrosis awareness month. Cystic fibrosis (CF) is an autosomal recessive genetic disorder. I chose 3 links of CF to share with you today:\" \/>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/mindthegraph.com\/blog\/ro\/fibroza-chistica\/\" \/>\n<meta property=\"og:locale\" content=\"ro_RO\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Cystic fibrosis awareness month - Mind the Graph Blog\" \/>\n<meta property=\"og:description\" content=\"May is the cystic fibrosis awareness month. Cystic fibrosis (CF) is an autosomal recessive genetic disorder. I chose 3 links of CF to share with you today:\" \/>\n<meta property=\"og:url\" content=\"https:\/\/mindthegraph.com\/blog\/ro\/fibroza-chistica\/\" \/>\n<meta property=\"og:site_name\" content=\"Mind the Graph Blog\" \/>\n<meta property=\"article:published_time\" content=\"2018-05-27T19:44:24+00:00\" \/>\n<meta property=\"article:modified_time\" content=\"2022-10-18T17:37:51+00:00\" \/>\n<meta property=\"og:image\" content=\"https:\/\/mindthegraph.com\/blog\/wp-content\/uploads\/2018\/05\/31846788804_1d47e5b32b_b_0.jpg\" \/>\n\t<meta property=\"og:image:width\" content=\"800\" \/>\n\t<meta property=\"og:image:height\" content=\"420\" \/>\n\t<meta property=\"og:image:type\" content=\"image\/jpeg\" \/>\n<meta name=\"author\" content=\"Fabiola Soares\" \/>\n<meta name=\"twitter:card\" content=\"summary_large_image\" \/>\n<meta name=\"twitter:label1\" content=\"Written by\" \/>\n\t<meta name=\"twitter:data1\" content=\"Fabiola Soares\" \/>\n\t<meta name=\"twitter:label2\" content=\"Est. reading time\" \/>\n\t<meta name=\"twitter:data2\" content=\"3 minutes\" \/>\n<!-- \/ Yoast SEO plugin. -->","yoast_head_json":{"title":"Cystic fibrosis awareness month - Mind the Graph Blog","description":"May is the cystic fibrosis awareness month. Cystic fibrosis (CF) is an autosomal recessive genetic disorder. I chose 3 links of CF to share with you today:","robots":{"index":"index","follow":"follow","max-snippet":"max-snippet:-1","max-image-preview":"max-image-preview:large","max-video-preview":"max-video-preview:-1"},"canonical":"https:\/\/mindthegraph.com\/blog\/ro\/fibroza-chistica\/","og_locale":"ro_RO","og_type":"article","og_title":"Cystic fibrosis awareness month - Mind the Graph Blog","og_description":"May is the cystic fibrosis awareness month. Cystic fibrosis (CF) is an autosomal recessive genetic disorder. I chose 3 links of CF to share with you today:","og_url":"https:\/\/mindthegraph.com\/blog\/ro\/fibroza-chistica\/","og_site_name":"Mind the Graph Blog","article_published_time":"2018-05-27T19:44:24+00:00","article_modified_time":"2022-10-18T17:37:51+00:00","og_image":[{"width":800,"height":420,"url":"https:\/\/mindthegraph.com\/blog\/wp-content\/uploads\/2018\/05\/31846788804_1d47e5b32b_b_0.jpg","type":"image\/jpeg"}],"author":"Fabiola Soares","twitter_card":"summary_large_image","twitter_misc":{"Written by":"Fabiola Soares","Est. reading time":"3 minutes"},"schema":{"@context":"https:\/\/schema.org","@graph":[{"@type":"WebPage","@id":"https:\/\/mindthegraph.com\/blog\/cystic-fibrosis\/","url":"https:\/\/mindthegraph.com\/blog\/cystic-fibrosis\/","name":"Cystic fibrosis awareness month - Mind the Graph Blog","isPartOf":{"@id":"https:\/\/mindthegraph.com\/blog\/#website"},"datePublished":"2018-05-27T19:44:24+00:00","dateModified":"2022-10-18T17:37:51+00:00","author":{"@id":"https:\/\/mindthegraph.com\/blog\/#\/schema\/person\/5592c012d89648325be9b0f3c3f91132"},"description":"May is the cystic fibrosis awareness month. Cystic fibrosis (CF) is an autosomal recessive genetic disorder. I chose 3 links of CF to share with you today:","breadcrumb":{"@id":"https:\/\/mindthegraph.com\/blog\/cystic-fibrosis\/#breadcrumb"},"inLanguage":"ro-RO","potentialAction":[{"@type":"ReadAction","target":["https:\/\/mindthegraph.com\/blog\/cystic-fibrosis\/"]}]},{"@type":"BreadcrumbList","@id":"https:\/\/mindthegraph.com\/blog\/cystic-fibrosis\/#breadcrumb","itemListElement":[{"@type":"ListItem","position":1,"name":"Home","item":"https:\/\/mindthegraph.com\/blog\/"},{"@type":"ListItem","position":2,"name":"Cystic fibrosis awareness month"}]},{"@type":"WebSite","@id":"https:\/\/mindthegraph.com\/blog\/#website","url":"https:\/\/mindthegraph.com\/blog\/","name":"Mind the Graph Blog","description":"Your science can be beautiful!","potentialAction":[{"@type":"SearchAction","target":{"@type":"EntryPoint","urlTemplate":"https:\/\/mindthegraph.com\/blog\/?s={search_term_string}"},"query-input":"required name=search_term_string"}],"inLanguage":"ro-RO"},{"@type":"Person","@id":"https:\/\/mindthegraph.com\/blog\/#\/schema\/person\/5592c012d89648325be9b0f3c3f91132","name":"Fabiola Soares","image":{"@type":"ImageObject","inLanguage":"ro-RO","@id":"https:\/\/mindthegraph.com\/blog\/#\/schema\/person\/image\/","url":"https:\/\/secure.gravatar.com\/avatar\/7dca2c6a766aff1db898cc74c18284d8?s=96&d=mm&r=g","contentUrl":"https:\/\/secure.gravatar.com\/avatar\/7dca2c6a766aff1db898cc74c18284d8?s=96&d=mm&r=g","caption":"Fabiola Soares"},"url":"https:\/\/mindthegraph.com\/blog\/ro\/author\/fabiola\/"}]}},"_links":{"self":[{"href":"https:\/\/mindthegraph.com\/blog\/ro\/wp-json\/wp\/v2\/posts\/7891"}],"collection":[{"href":"https:\/\/mindthegraph.com\/blog\/ro\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/mindthegraph.com\/blog\/ro\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/mindthegraph.com\/blog\/ro\/wp-json\/wp\/v2\/users\/11"}],"replies":[{"embeddable":true,"href":"https:\/\/mindthegraph.com\/blog\/ro\/wp-json\/wp\/v2\/comments?post=7891"}],"version-history":[{"count":12,"href":"https:\/\/mindthegraph.com\/blog\/ro\/wp-json\/wp\/v2\/posts\/7891\/revisions"}],"predecessor-version":[{"id":23501,"href":"https:\/\/mindthegraph.com\/blog\/ro\/wp-json\/wp\/v2\/posts\/7891\/revisions\/23501"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/mindthegraph.com\/blog\/ro\/wp-json\/wp\/v2\/media\/7919"}],"wp:attachment":[{"href":"https:\/\/mindthegraph.com\/blog\/ro\/wp-json\/wp\/v2\/media?parent=7891"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/mindthegraph.com\/blog\/ro\/wp-json\/wp\/v2\/categories?post=7891"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/mindthegraph.com\/blog\/ro\/wp-json\/wp\/v2\/tags?post=7891"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}