{"id":7891,"date":"2018-05-27T16:44:24","date_gmt":"2018-05-27T19:44:24","guid":{"rendered":"https:\/\/blog.mindthegraph.com\/?p=7891"},"modified":"2022-10-18T14:37:51","modified_gmt":"2022-10-18T17:37:51","slug":"cystic-fibrosis","status":"publish","type":"post","link":"https:\/\/mindthegraph.com\/blog\/lt\/cistine-fibroze\/","title":{"rendered":"Informuotumo apie cistin\u0119 fibroz\u0119 m\u0117nuo"},"content":{"rendered":"<p>Gegu\u017e\u0117 - cistin\u0117s fibroz\u0117s \u017einomumo m\u0117nuo. Cistin\u0117 fibroz\u0117 (CF) yra autosominis recesyvinis genetinis sutrikimas. CF sukelia cistin\u0117s fibroz\u0117s transmembraninio laidumo reguliatoriaus (CFTR) kanal\u0105 koduojan\u010dio geno mutacijos.  \u0160is baltymas yra atsakingas u\u017e jon\u0173 perne\u0161imo per l\u0105steli\u0173 membranas poky\u010dius.<\/p>\n\n\n\n<p>Pagal Genetikos nam\u0173 rekomendacijas <sup>1<\/sup>, CFTR genas pateikia nurodymus, kaip gaminti baltym\u0105, vadinam\u0105 cistin\u0117s fibroz\u0117s transmembraniniu laidumo reguliatoriumi:<\/p>\n\n\n\n<p>\u0160is baltymas veikia kaip kanalas per l\u0105steli\u0173, gaminan\u010di\u0173 gleives, prakait\u0105, seiles, a\u0161aras ir vir\u0161kinimo fermentus, membran\u0105. Kanalas perne\u0161a neigiamai \u012fkrautas daleles, vadinamas chlorido jonais, \u012f l\u0105steles ir i\u0161 j\u0173. Chlorido jon\u0173 perne\u0161imas padeda kontroliuoti vandens jud\u0117jim\u0105 audiniuose, kuris b\u016btinas plon\u0173, laisvai tekan\u010di\u0173 gleivi\u0173 gamybai. Gleiv\u0117s yra slidi med\u017eiaga, kuri sutepa ir apsaugo kv\u0117pavimo tak\u0173, vir\u0161kinimo sistemos, reprodukcin\u0117s sistemos ir kit\u0173 organ\u0173 bei audini\u0173 gleivin\u0119.<\/p>\n\n\n\n<p><span style=\"font-weight: 400;\">CFTR baltymas taip pat reguliuoja kit\u0173 kanal\u0173, pavyzd\u017eiui, teigiamai \u012fkraut\u0173 daleli\u0173, vadinam\u0173 natrio jonais, perne\u0161im\u0105 per l\u0105steli\u0173 membranas, funkcij\u0105. \u0160ie kanalai b\u016btini normaliai toki\u0173 organ\u0173, kaip plau\u010diai ir kasa, funkcijai u\u017etikrinti.<\/span><\/p>\n\n\n<div class=\"wp-block-image\">\n<figure class=\"aligncenter\"><a href=\"https:\/\/mindthegraph.com\/science_figures\" target=\"_blank\" rel=\"https:\/\/mindthegraph.com\/science_figures noopener\"><img decoding=\"async\" loading=\"lazy\" width=\"424\" height=\"306\" src=\"https:\/\/blog.mindthegraph.com\/wp-content\/uploads\/2018\/05\/dfaefqawefafc.png\" alt=\"dfaefqawefafc\" class=\"wp-image-7917\" srcset=\"https:\/\/mindthegraph.com\/blog\/wp-content\/uploads\/2018\/05\/dfaefqawefafc.png 424w, https:\/\/mindthegraph.com\/blog\/wp-content\/uploads\/2018\/05\/dfaefqawefafc-300x217.png 300w\" sizes=\"(max-width: 424px) 100vw, 424px\" \/><\/a><\/figure><\/div>\n\n\n<p>Tai turi \u012ftakos egzokrinini\u0173 liauk\u0173 veiklai, tod\u0117l susidaro tir\u0161tesn\u0117s, sunkiai pa\u0161alinamos med\u017eiagos (gleiv\u0117s, prakaitas arba kasos fermentai).<br>D\u0117l \u0161ios prie\u017easties cistin\u0117 fibroz\u0117 pa\u017eeid\u017eia vir\u0161kinimo ir kv\u0117pavimo sistemas bei prakaito liaukas.<\/p>\n\n\n\n<p>Ta\u010diau liga labiausiai pa\u017eeid\u017eia kv\u0117pavimo sistem\u0105. Plau\u010diuose gaminasi tir\u0161tos gleiv\u0117s, kurios gali \u012fstrigti kv\u0117pavimo takuose. Cistine fibroze sergantiems pacientams gali i\u0161sivystyti l\u0117tin\u0117s bakterin\u0117s plau\u010di\u0173 infekcijos ir u\u017edegimas, galiausiai galintis sukelti galutin\u0119 plau\u010di\u0173 ligos stadij\u0105.<br>Kiti simptomai yra kosulys su sekretu, pasikartojantis plau\u010di\u0173 u\u017edegimas ir l\u0117tinis bronchitas.<\/p>\n\n\n\n<p>CF sergan\u010dioms moterims sunkiau pastoti, nes d\u0117l tir\u0161tesni\u0173 gimdos kaklelio gleivi\u0173 spermatozoidams sunkiau prasiskverbti. Vyrams dar sunkiau. Apie 98% vyr\u0173 yra nevaisingi, nors j\u0173 lytinis paj\u0117gumas ir potencija yra visi\u0161kai normal\u016bs.<\/p>\n\n\n\n<p>\u0160iandien pasirinkau 3 CF nuorodas, kuriomis noriu su jumis pasidalyti.<\/p>\n\n\n\n<div class=\"is-content-justification-center is-layout-flex wp-container-1 wp-block-buttons\">\n<div class=\"wp-block-button\"><a class=\"wp-block-button__link\" href=\"https:\/\/mindthegraph.com\/science_figures\">Per kelias minutes sukurkite efektyvius mokslinius paveiksl\u0117lius<\/a><\/div>\n<\/div>\n\n\n\n<h3>Geras bendravimas, demistifikuojantis cistin\u0119 fibroz\u0119<\/h3>\n\n\n\n<center>\n<p><\/p><\/center>\n\n\n<p><iframe loading=\"lazy\" title=\"Kas yra cistin\u0117 fibroz\u0117?\" width=\"800\" height=\"450\" src=\"https:\/\/www.youtube.com\/embed\/k4U5wyPzxJE?feature=oembed\" frameborder=\"0\" allow=\"accelerometer; autoplay; clipboard-write; encrypted-media; gyroscope; picture-in-picture\" allowfullscreen><\/iframe><\/p>\n\n\n\n<h3>15 dalyk\u0173, kuriuos nori, kad \u017einotum\u0117te apie cistine fibroze sergan\u010dius \u017emones - the buzzfeed list<\/h3>\n\n\n\n<p>Gyventi sergant CF n\u0117ra lengva, tod\u0117l labai svarbu tur\u0117ti palaikym\u0105 ir kalb\u0117tis apie tai. Per\u017ei\u016br\u0117kite \u0161\u012f buzzfeed s\u0105ra\u0161\u0105<sup>2<\/sup> , kad pamatytum\u0117te, kaip cistine fibroze sergantys \u017emon\u0117s pasakoja apie savo kasdienyb\u0119.<\/p>\n\n\n\n<div class=\"is-content-justification-center is-layout-flex wp-container-2 wp-block-buttons\">\n<div class=\"wp-block-button\"><a class=\"wp-block-button__link\" href=\"https:\/\/mindthegraph.com\/science_figures\">Prad\u0117kite naudotis \"Mind The Graph\" dabar nemokamai!<\/a><\/div>\n<\/div>\n\n\n\n<h3>&nbsp;Dant\u0173 pastoje esantis antibakterinis junginys<sup>3<\/sup>, vadinamo triklozanu, gali b\u016bti b\u016bsimo cistin\u0117s fibroz\u0117s (CF) gydymo dalis.<\/h3>\n\n\n<div class=\"wp-block-image size-full wp-image-7921\">\n<figure class=\"aligncenter\"><a href=\"https:\/\/mindthegraph.com\/science_figures\" target=\"_blank\" rel=\"https:\/\/mindthegraph.com\/science_figures noopener\"><img decoding=\"async\" loading=\"lazy\" width=\"800\" height=\"420\" src=\"https:\/\/blog.mindthegraph.com\/wp-content\/uploads\/2018\/05\/31846788804_1d47e5b32b_b_0-1.jpg\" alt=\"\u0160iame paveiksl\u0117lyje matyti sud\u0117tinga milijon\u0173 vienal\u0105s\u010di\u0173 bakterij\u0173 Pseudomonas aeruginosa kolonija.\" class=\"wp-image-7921\" srcset=\"https:\/\/mindthegraph.com\/blog\/wp-content\/uploads\/2018\/05\/31846788804_1d47e5b32b_b_0-1.jpg 800w, https:\/\/mindthegraph.com\/blog\/wp-content\/uploads\/2018\/05\/31846788804_1d47e5b32b_b_0-1-300x158.jpg 300w, https:\/\/mindthegraph.com\/blog\/wp-content\/uploads\/2018\/05\/31846788804_1d47e5b32b_b_0-1-768x403.jpg 768w\" sizes=\"(max-width: 800px) 100vw, 800px\" \/><\/a><figcaption>\u0160iame paveiksl\u0117lyje matyti sud\u0117tinga milijon\u0173 vienal\u0105s\u010di\u0173 bakterij\u0173 Pseudomonas aeruginosa kolonija.<\/figcaption><\/figure><\/div>\n\n\n<p>Tyrimas&nbsp;<strong><em>Triklozanas yra aminoglikozid\u0173 pagalbin\u0117 med\u017eiaga, skirta Pseudomonas aeruginosa biopl\u0117vel\u0117ms naikinti <sup>4<\/sup>&nbsp;<\/em><\/strong>rodo, kad \u0161is derinys padidina P. aeruginosa biofilm\u0173 l\u0105steli\u0173 naikinimo greit\u012f ir laipsn\u012f, o tai turi svarbi\u0105 klinikin\u0119 reik\u0161m\u0119 gydant CF sergan\u010di\u0173 pacient\u0173 biofilm\u0173 infekcijas.<\/p>\n\n\n\n<ol><li><a href=\"https:\/\/medlineplus.gov\/genetics\/gene\/cftr\/\" target=\"_blank\" rel=\"noreferrer noopener\">CFTR genas cistin\u0117s fibroz\u0117s transmembraninio laidumo reguliatorius.<\/a><\/li><li><a href=\"https:\/\/www.buzzfeed.com\/ailbhemalone\/living-with-cystic-fibrosis?utm_term=.srElmo7oO#.nyQVXbMb2\" target=\"_blank\" rel=\"noreferrer noopener\">15 dalyk\u0173, kuriuos \u017emon\u0117s, sergantys cistine fibroze, nori, kad \u017einotum\u0117te.<\/a><\/li><li><a href=\"https:\/\/cysticfibrosisnewstoday.com\/2018\/05\/21\/cystic-fibrosis-antiobiotic-more-effective-in-combo-with-toothpaste-antibacterial-study-suggests\/\" target=\"_blank\" rel=\"noreferrer noopener\">Tyrimas rodo, kad dant\u0173 pastoje esantis antibakterinis preparatas triklozanas gerai veikia kaip kombinuotas gydymas antibiotikais.<\/a><\/li><li><a href=\"https:\/\/journals.asm.org\/doi\/full\/10.1128\/AAC.00146-18\" target=\"_blank\" rel=\"noreferrer noopener\">Triklozanas yra aminoglikozid\u0173 pagalbin\u0117 med\u017eiaga, skirta i\u0161naikinti&nbsp;<em>Pseudomonas aeruginosa<\/em>&nbsp;Biofilmai.<\/a><\/li><\/ol>","protected":false},"excerpt":{"rendered":"<p>Gegu\u017e\u0117 - cistin\u0117s fibroz\u0117s \u017einomumo m\u0117nuo. Cistin\u0117 fibroz\u0117 (CF) yra autosominis recesyvinis genetinis sutrikimas. CF sukelia cistin\u0117s fibroz\u0117s transmembraninio laidumo reguliatoriaus (CFTR) kanal\u0105 koduojan\u010dio geno mutacijos.  \u0160is baltymas yra atsakingas u\u017e jon\u0173 perne\u0161imo per l\u0105steli\u0173 membranas poky\u010dius. Pagal Genetikos nam\u0173 nuorodas 1, CFTR genas u\u017etikrina [...]<\/p>","protected":false},"author":11,"featured_media":7919,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"image","meta":[],"categories":[959,28],"tags":[554,250],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v19.9 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Cystic fibrosis awareness month - Mind the Graph Blog<\/title>\n<meta name=\"description\" content=\"May is the cystic fibrosis awareness month. Cystic fibrosis (CF) is an autosomal recessive genetic disorder. I chose 3 links of CF to share with you today:\" \/>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/mindthegraph.com\/blog\/lt\/cistine-fibroze\/\" \/>\n<meta property=\"og:locale\" content=\"lt_LT\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Cystic fibrosis awareness month - Mind the Graph Blog\" \/>\n<meta property=\"og:description\" content=\"May is the cystic fibrosis awareness month. Cystic fibrosis (CF) is an autosomal recessive genetic disorder. 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