{"id":7891,"date":"2018-05-27T16:44:24","date_gmt":"2018-05-27T19:44:24","guid":{"rendered":"https:\/\/blog.mindthegraph.com\/?p=7891"},"modified":"2022-10-18T14:37:51","modified_gmt":"2022-10-18T17:37:51","slug":"cystic-fibrosis","status":"publish","type":"post","link":"https:\/\/mindthegraph.com\/blog\/et\/tsustiline-fibroos\/","title":{"rendered":"Ts\u00fcstilise fibroosi teadlikkuse kuu"},"content":{"rendered":"<p>Mai on ts\u00fcstilise fibroosi teadlikkuse kuu. Ts\u00fcstiline fibroos (CF) on autosoomne retsessiivne geneetiline haigus. CF on p\u00f5hjustatud ts\u00fcstilise fibroosi transmembraanjuhtivuse regulaatorit (CFTR) kodeeriva geeni mutatsioonidest.  See valk vastutab ioonitranspordi muutuse eest l\u00e4bi rakumembraanide.<\/p>\n\n\n\n<p>Vastavalt geneetilistele kodustele viidetele <sup>1<\/sup>CFTR-geen annab juhiseid valgu, nn ts\u00fcstilise fibroosi transmembraanjuhtivuse regulaatori valmistamiseks:<\/p>\n\n\n\n<p>See valk toimib lima, higi, s\u00fclje, pisarate ja seedeens\u00fc\u00fcmide tootmise rakumembraanide kanalina. Kanal transpordib negatiivselt laetud osakesi, mida nimetatakse kloriidioonideks, rakkudesse ja rakkudest v\u00e4lja. Kloriidioonide transport aitab kontrollida vee liikumist kudedes, mis on vajalik \u00f5hukese, vabalt voolava lima tootmiseks. Lima on libe aine, mis m\u00e4\u00e4rib ja kaitseb hingamisteede, seedes\u00fcsteemi, reproduktiivs\u00fcsteemi ja muude organite ja kudede limaskesta.<\/p>\n\n\n\n<p><span style=\"font-weight: 400;\">CFTR-valk reguleerib ka teiste kanalite, n\u00e4iteks nende, mis transpordivad positiivselt laetud osakesi, mida nimetatakse naatriumioonideks, l\u00e4bi rakumembraanide. Need kanalid on vajalikud selliste organite nagu kopsud ja k\u00f5hun\u00e4\u00e4re normaalseks toimimiseks.<\/span><\/p>\n\n\n<div class=\"wp-block-image\">\n<figure class=\"aligncenter\"><a href=\"https:\/\/mindthegraph.com\/science_figures\" target=\"_blank\" rel=\"https:\/\/mindthegraph.com\/science_figures noopener\"><img decoding=\"async\" loading=\"lazy\" width=\"424\" height=\"306\" src=\"https:\/\/blog.mindthegraph.com\/wp-content\/uploads\/2018\/05\/dfaefqawefafc.png\" alt=\"dfaefqawefafc\" class=\"wp-image-7917\" srcset=\"https:\/\/mindthegraph.com\/blog\/wp-content\/uploads\/2018\/05\/dfaefqawefafc.png 424w, https:\/\/mindthegraph.com\/blog\/wp-content\/uploads\/2018\/05\/dfaefqawefafc-300x217.png 300w\" sizes=\"(max-width: 424px) 100vw, 424px\" \/><\/a><\/figure><\/div>\n\n\n<p>See m\u00f5jutab eksokriinsete n\u00e4\u00e4rmete t\u00f6\u00f6d, tekitades paksemaid, raskesti eemaldatavaid aineid (lima, higi v\u00f5i k\u00f5hun\u00e4\u00e4rmeens\u00fc\u00fcmid).<br>Selle t\u00f5ttu m\u00f5jutab ts\u00fcstiline fibroos seede- ja hingamiss\u00fcsteemi ning higin\u00e4\u00e4rmeid.<\/p>\n\n\n\n<p>K\u00f5ige enam m\u00f5jutab haigus siiski hingamisteid. Kopsud toodavad paksu lima, mis v\u00f5ib j\u00e4\u00e4da hingamisteedesse kinni. Ts\u00fcstilise fibroosiga patsientidel v\u00f5ivad tekkida kroonilised bakteriaalsed kopsuinfektsioonid ja p\u00f5letikud, mis v\u00f5ivad l\u00f5puks p\u00f5hjustada l\u00f5ppstaadiumis kopsuhaigust.<br>Muud s\u00fcmptomid on eritumisega k\u00f6ha, korduv kopsup\u00f5letik ja krooniline bronhiit.<\/p>\n\n\n\n<p>CF-ga naistel on raskem rasestuda, sest paksem emakakaela lima raskendab sperma l\u00e4bip\u00e4\u00e4su. Meestel on see veelgi raskem. Ligikaudu 98% meestest on steriilsed, kuigi nende seksuaaltervis ja potentsus on t\u00e4iesti normaalne.<\/p>\n\n\n\n<p>Valisin t\u00e4na teiega jagamiseks 3 CF-i linki.<\/p>\n\n\n\n<div class=\"is-content-justification-center is-layout-flex wp-container-1 wp-block-buttons\">\n<div class=\"wp-block-button\"><a class=\"wp-block-button__link\" href=\"https:\/\/mindthegraph.com\/science_figures\">Loo efektiivseid teadusfiguurid minutitega<\/a><\/div>\n<\/div>\n\n\n\n<h3>Hea teatis, mis dem\u00fcstifitseerib ts\u00fcstilise fibroosi<\/h3>\n\n\n\n<center>\n<p><\/p><\/center>\n\n\n<p><iframe loading=\"lazy\" title=\"Mis on ts\u00fcstiline fibroos?\" width=\"800\" height=\"450\" src=\"https:\/\/www.youtube.com\/embed\/k4U5wyPzxJE?feature=oembed\" frameborder=\"0\" allow=\"accelerometer; autoplay; clipboard-write; encrypted-media; gyroscope; picture-in-picture\" allowfullscreen><\/iframe><\/p>\n\n\n\n<h3>15 asja, mida ts\u00fcstilise fibroosiga inimesed tahavad, et te teaksite - buzzfeed list<\/h3>\n\n\n\n<p>CF-ga elamine ei ole lihtne, seega on v\u00e4ga oluline, et meil oleks toetust ja et me r\u00e4\u00e4giksime sellest. Vaadake seda buzzfeedi nimekirja<sup>2<\/sup> , et n\u00e4ha ts\u00fcstilise fibroosiga inimesi, kes r\u00e4\u00e4givad oma rutiinist.<\/p>\n\n\n\n<div class=\"is-content-justification-center is-layout-flex wp-container-2 wp-block-buttons\">\n<div class=\"wp-block-button\"><a class=\"wp-block-button__link\" href=\"https:\/\/mindthegraph.com\/science_figures\">Alusta kohe tasuta Mind The Graphi kasutamist!<\/a><\/div>\n<\/div>\n\n\n\n<h3>&nbsp;Antibakteriaalne \u00fchend, mida leidub hambapastas.<sup>3<\/sup>, mida nimetatakse triklosaaniks, v\u00f5ib tulevikus olla osa ts\u00fcstilise fibroosi (CF) ravist.<\/h3>\n\n\n<div class=\"wp-block-image size-full wp-image-7921\">\n<figure class=\"aligncenter\"><a href=\"https:\/\/mindthegraph.com\/science_figures\" target=\"_blank\" rel=\"https:\/\/mindthegraph.com\/science_figures noopener\"><img decoding=\"async\" loading=\"lazy\" width=\"800\" height=\"420\" src=\"https:\/\/blog.mindthegraph.com\/wp-content\/uploads\/2018\/05\/31846788804_1d47e5b32b_b_0-1.jpg\" alt=\"Sellel pildil on kujutatud miljonite \u00fche rakulise bakteri Pseudomonas aeruginosa keerukas koloonia.\" class=\"wp-image-7921\" srcset=\"https:\/\/mindthegraph.com\/blog\/wp-content\/uploads\/2018\/05\/31846788804_1d47e5b32b_b_0-1.jpg 800w, https:\/\/mindthegraph.com\/blog\/wp-content\/uploads\/2018\/05\/31846788804_1d47e5b32b_b_0-1-300x158.jpg 300w, https:\/\/mindthegraph.com\/blog\/wp-content\/uploads\/2018\/05\/31846788804_1d47e5b32b_b_0-1-768x403.jpg 768w\" sizes=\"(max-width: 800px) 100vw, 800px\" \/><\/a><figcaption>Sellel pildil on kujutatud miljonite \u00fche rakulise bakteri Pseudomonas aeruginosa keerukas koloonia.<\/figcaption><\/figure><\/div>\n\n\n<p>Uuringud&nbsp;<strong><em>Triklosaan on aminogl\u00fckosiidi adjuvant Pseudomonas aeruginosa biokilede likvideerimiseks. <sup>4<\/sup>&nbsp;<\/em><\/strong>n\u00e4itavad, et see kombinatsioon suurendab nii P. aeruginosa biokilede rakkude tapmise kiirust kui ka m\u00e4\u00e4ra, millel on oluline kliiniline m\u00f5ju CF-patsientide biokileinfektsioonide ravile.<\/p>\n\n\n\n<ol><li><a href=\"https:\/\/medlineplus.gov\/genetics\/gene\/cftr\/\" target=\"_blank\" rel=\"noreferrer noopener\">CFTR geen ts\u00fcstilise fibroosi transmembraanjuhtivuse regulaator.<\/a><\/li><li><a href=\"https:\/\/www.buzzfeed.com\/ailbhemalone\/living-with-cystic-fibrosis?utm_term=.srElmo7oO#.nyQVXbMb2\" target=\"_blank\" rel=\"noreferrer noopener\">15 asja, mida ts\u00fcstilise fibroosiga inimesed tahavad, et te teaksite.<\/a><\/li><li><a href=\"https:\/\/cysticfibrosisnewstoday.com\/2018\/05\/21\/cystic-fibrosis-antiobiotic-more-effective-in-combo-with-toothpaste-antibacterial-study-suggests\/\" target=\"_blank\" rel=\"noreferrer noopener\">Triklosaan, antibakteriaalne hambapasta, toimib h\u00e4sti kui kombineeritud antibiootikumide ravi, uuring n\u00e4itab.<\/a><\/li><li><a href=\"https:\/\/journals.asm.org\/doi\/full\/10.1128\/AAC.00146-18\" target=\"_blank\" rel=\"noreferrer noopener\">Triklosaan on aminogl\u00fckosiidi adjuvant likvideerimiseks&nbsp;<em>Pseudomonas aeruginosa<\/em>&nbsp;Biokiled.<\/a><\/li><\/ol>","protected":false},"excerpt":{"rendered":"<p>Mai on ts\u00fcstilise fibroosi teadlikkuse kuu. Ts\u00fcstiline fibroos (CF) on autosoomne retsessiivne geneetiline haigus. CF on p\u00f5hjustatud ts\u00fcstilise fibroosi transmembraanjuhtivuse regulaatorit (CFTR) kodeeriva geeni mutatsioonidest.  See valk vastutab ioonitranspordi muutuse eest l\u00e4bi rakumembraanide. Vastavalt Genetics home viited 1, CFTR geeni annab [...]<\/p>","protected":false},"author":11,"featured_media":7919,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"image","meta":[],"categories":[959,28],"tags":[554,250],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v19.9 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Cystic fibrosis awareness month - Mind the Graph Blog<\/title>\n<meta name=\"description\" content=\"May is the cystic fibrosis awareness month. Cystic fibrosis (CF) is an autosomal recessive genetic disorder. I chose 3 links of CF to share with you today:\" \/>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/mindthegraph.com\/blog\/et\/tsustiline-fibroos\/\" \/>\n<meta property=\"og:locale\" content=\"et_EE\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Cystic fibrosis awareness month - Mind the Graph Blog\" \/>\n<meta property=\"og:description\" content=\"May is the cystic fibrosis awareness month. Cystic fibrosis (CF) is an autosomal recessive genetic disorder. 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