{"id":25947,"date":"2022-12-15T16:05:32","date_gmt":"2022-12-15T19:05:32","guid":{"rendered":"https:\/\/mindthegraph.com\/blog\/review-paper-vs-research-paper-copy\/"},"modified":"2022-12-21T16:11:05","modified_gmt":"2022-12-21T19:11:05","slug":"stiff-person-syndrome","status":"publish","type":"post","link":"https:\/\/mindthegraph.com\/blog\/cs\/stiff-person-syndrome\/","title":{"rendered":"Syndrom ztuhl\u00e9 osoby: P\u0159\u00edznaky, p\u0159\u00ed\u010diny a l\u00e9\u010dba"},"content":{"rendered":"<p>Den co den jsme z\u00e1visl\u00ed na na\u0161ich svalech, kter\u00e9 n\u00e1m pom\u00e1haj\u00ed dr\u017eet k\u00e1vu, pracovat na notebooku a chodit na proch\u00e1zky. I kdy\u017e je to neobvykl\u00e9, tyto svaly n\u00e1s n\u011bkdy mohou zklamat.<\/p>\n\n\n\n<p>V\u0161echny tyto povinnosti jsou ohro\u017eeny autoimunitn\u00edm a neurologick\u00fdm onemocn\u011bn\u00edm. \u010ct\u011bte d\u00e1le a dozv\u00edte se v\u00edce o t\u00e9to mimo\u0159\u00e1dn\u011b vz\u00e1cn\u00e9 poru\u0161e.<\/p>\n\n\n\n<h2>Co je to syndrom ztuhlosti?<\/h2>\n\n\n\n<p>Podle N\u00e1rodn\u00edho institutu pro neurologick\u00e9 poruchy a mrtvici (National Institute of Neurological Disorders and Stroke) je syndrom ztuhlosti, zn\u00e1m\u00fd tak\u00e9 jako Moersch-Woltman\u016fv syndrom, vz\u00e1cn\u00e9 neurologick\u00e9 onemocn\u011bn\u00ed s autoimunitn\u00edmi rysy.&nbsp;<\/p>\n\n\n\n<p>T\u011blo je v d\u016fsledku tohoto onemocn\u011bn\u00ed ztuhl\u00e9 a citliv\u011bj\u0161\u00ed na zvuky, kontakt a emocion\u00e1ln\u00ed stres. Podle instituce m\u016f\u017ee tato zv\u00fd\u0161en\u00e1 citlivost vy\u00fastit krom\u011b shrben\u00fdch a napjat\u00fdch postoj\u016f tak\u00e9 ve svalov\u00e9 k\u0159e\u010de.<\/p>\n\n\n\n<p>Podle Nadace pro v\u00fdzkum syndromu ztuhlosti mohou b\u00fdt svalov\u00e9 k\u0159e\u010de tak siln\u00e9, \u017ee mohou vykloubit klouby a mo\u017en\u00e1 i zlomit kosti.<\/p>\n\n\n\n<p><strong>Pouze jeden nebo dva lid\u00e9 z milionu<\/strong> trp\u00ed syndromem ztuhlosti, uv\u00e1d\u00ed John Hopkins Medicine. Syndrom ztuhlosti postihuje dvakr\u00e1t v\u00edce \u017een ne\u017e mu\u017e\u016f. P\u0159\u00edznaky se mohou objevit v jak\u00e9mkoli v\u011bku, nej\u010dast\u011bji se v\u0161ak vyskytuj\u00ed mezi 30. a 60. rokem \u017eivota.<\/p>\n\n\n\n<h2>P\u0159\u00edznaky a p\u0159\u00ed\u010diny syndromu ztuhl\u00e9 osoby<\/h2>\n\n\n\n<h3>P\u0159\u00edznaky<\/h3>\n\n\n\n<p>Nejv\u00fdznamn\u011bj\u0161\u00edm aspektem tohoto syndromu, kter\u00fd je t\u0159eba zd\u016fraznit, je to, jak je neobvykl\u00fd a jak na n\u011bj reaguj\u00ed r\u016fzn\u00ed jedinci; je velmi b\u011b\u017en\u00e9, \u017ee n\u011bkte\u0159\u00ed pacienti z\u016fst\u00e1vaj\u00ed stabiln\u00ed po cel\u00e1 l\u00e9ta, zat\u00edmco u jin\u00fdch se stav rychle zhor\u0161uje.<\/p>\n\n\n\n<p>U v\u011bt\u0161iny pacient\u016f jako prvn\u00ed ztuhnou a rozt\u00e1hnou se svaly trupu a b\u0159icha. N\u00e1sledn\u011b se obvykle objev\u00ed n\u00e1sleduj\u00edc\u00ed p\u0159\u00edznaky:&nbsp;<\/p>\n\n\n\n<ul>\n<li>Bolest;<\/li>\n\n\n\n<li>Svalov\u00e1 ztuhlost p\u0159ich\u00e1z\u00ed a odch\u00e1z\u00ed;<\/li>\n\n\n\n<li>Bolestiv\u00e9 pot\u00ed\u017ee;<\/li>\n\n\n\n<li>Svaly nohou \u010dasem ztuhnou, stejn\u011b jako ostatn\u00ed svaly v cel\u00e9m t\u011ble;<\/li>\n\n\n\n<li>Shrben\u00e9 dr\u017een\u00ed t\u011bla;<\/li>\n\n\n\n<li>Obt\u00ed\u017en\u00e1 ch\u016fze nebo pohyb z d\u016fvodu ztuhlosti;<\/li>\n\n\n\n<li>Dlouh\u00e9 svalov\u00e9 k\u0159e\u010de, kter\u00e9 mohou trvat n\u011bkolik sekund, minut nebo hodin.&nbsp;<\/li>\n<\/ul>\n\n\n\n<h3>P\u0159\u00ed\u010diny<\/h3>\n\n\n\n<p>P\u0159esto\u017ee nebyla zji\u0161t\u011bna p\u0159\u00ed\u010dina syndromu ztuhlosti, v\u011bdci se domn\u00edvaj\u00ed, \u017ee jde o autoimunitn\u00ed poruchu, kter\u00e1 zp\u016fsobuje, \u017ee imunitn\u00ed syst\u00e9m ni\u010d\u00ed zdrav\u00e9 bu\u0148ky. Jedinci s t\u00edmto onemocn\u011bn\u00edm produkuj\u00ed protil\u00e1tky, kter\u00e9 napadaj\u00ed enzym dekarboxyl\u00e1zu kyseliny glutamov\u00e9 (GAD).<\/p>\n\n\n\n<p>Tento enzym je nezbytn\u00fd pro tvorbu kyseliny gama-aminom\u00e1seln\u00e9 (GABA), neurotransmiteru, kter\u00fd pom\u00e1h\u00e1 p\u0159i svalov\u00e9 koordinaci. C\u00edlen\u00e9 p\u016fsoben\u00ed na GAD sni\u017euje mno\u017estv\u00ed GABA v t\u011ble.<\/p>\n\n\n\n<p>P\u0159esto nen\u00ed funkce GAD p\u0159i vzniku a progresi syndromu ztuhlosti zcela zn\u00e1ma. N\u011bkte\u0159\u00ed jedinci s t\u00edmto onemocn\u011bn\u00edm ve skute\u010dnosti nemaj\u00ed detekovateln\u00e9 protil\u00e1tky proti GAD.<\/p>\n\n\n\n<p>Dal\u0161\u00edm v\u00fdznamn\u00fdm faktorem, kter\u00fd m\u016f\u017ee p\u0159isp\u00edvat k v\u00fdskytu tohoto onemocn\u011bn\u00ed, je skute\u010dnost, \u017ee u lid\u00ed se syndromem ztuhlosti se m\u00e9n\u011b \u010dasto vyskytuje b\u00edlkovina zvan\u00e1 amfifyzin. Tento protein je nezbytn\u00fd pro vz\u00e1jemnou interakci nervov\u00fdch bun\u011bk a nach\u00e1z\u00ed se v nervov\u00fdch zakon\u010den\u00edch.<\/p>\n\n\n\n<h2>Jak se diagnostikuje a l\u00e9\u010d\u00ed syndrom ztuhlosti?<\/h2>\n\n\n\n<h3>Diagnostika<\/h3>\n\n\n\n<p>P\u0159\u00edznaky syndromu ztuhlosti jsou srovnateln\u00e9 s p\u0159\u00edznaky jin\u00fdch onemocn\u011bn\u00ed, jako je tetanus, roztrou\u0161en\u00e1 skler\u00f3za a svalov\u00e9 dystrofie. \u010casto b\u00fdv\u00e1 myln\u011b pova\u017eov\u00e1n za jin\u00e9 autoimunitn\u00ed onemocn\u011bn\u00ed, jako je Parkinsonova choroba nebo kombinace \u00fazkosti a fobie.<\/p>\n\n\n\n<p>Zdravotnick\u00fd pracovn\u00edk m\u016f\u017ee prov\u00e9st n\u011bkolik test\u016f, aby vylou\u010dil tyto poruchy a zkontroloval, zda se nejedn\u00e1 o syndrom ztuhl\u00e9 osoby, nap\u0159.:<\/p>\n\n\n\n<ul>\n<li><strong>Krevn\u00ed test:<\/strong> testovat p\u0159\u00edtomnost protil\u00e1tek proti GAC nebo amfifyzinu, stejn\u011b jako dal\u0161\u00ed p\u0159\u00edznaky, kter\u00e9 by mohly nazna\u010dovat nebo vylou\u010dit jin\u00e9 poruchy.&nbsp;<\/li>\n\n\n\n<li><strong>Lumb\u00e1ln\u00ed punkce: <\/strong>Postup, p\u0159i kter\u00e9m se jehlou odeb\u00edr\u00e1 tekutina z p\u00e1te\u0159n\u00edho kan\u00e1lu a testuje se p\u0159\u00edtomnost protil\u00e1tek proti GAC nebo amfifyzinu, jako\u017e i dal\u0161\u00ed p\u0159\u00edznaky, kter\u00e9 mohou nazna\u010dovat nebo vylu\u010dovat jin\u00e9 poruchy.&nbsp;<\/li>\n\n\n\n<li><strong>Elektromyografie (EMG): <\/strong>P\u0159\u00edstroj detekuje prob\u00edhaj\u00edc\u00ed motorickou aktivitu sval\u016f m\u011b\u0159en\u00edm jejich elektrick\u00e9 aktivity.<\/li>\n<\/ul>\n\n\n\n<h2>L\u00e9\u010dba<\/h2>\n\n\n\n<p>O l\u00e9\u010db\u011b syndromu ztuhlosti se rozhoduje na z\u00e1klad\u011b p\u0159\u00edznak\u016f, p\u0159i\u010dem\u017e c\u00edlem je zm\u00edrnit p\u0159\u00edznaky a z\u00e1rove\u0148 zv\u00fd\u0161it kvalitu \u017eivota, nap\u0159\u00edklad pohyblivost a pohodl\u00ed.<\/p>\n\n\n\n<p>L\u00e9\u010dba m\u016f\u017ee zahrnovat:<\/p>\n\n\n\n<ul>\n<li>Benzodiazepiny, jako je diazepam a klonazepam nebo baklofen, k l\u00e9\u010db\u011b svalov\u00e9 ztuhlosti;&nbsp;<\/li>\n\n\n\n<li>&nbsp;L\u00e9ky proti z\u00e1chvat\u016fm, protiz\u00e1n\u011btliv\u00e9 l\u00e9ky a kortikosteroidy proti bolesti;<\/li>\n\n\n\n<li>Fyzik\u00e1ln\u00ed terapie;<\/li>\n\n\n\n<li>Mas\u00e1\u017ee;<\/li>\n\n\n\n<li>L\u00e9\u010dba vodou;<\/li>\n\n\n\n<li>Tepeln\u00e1 terapie;<\/li>\n\n\n\n<li>Akupunktura.<\/li>\n<\/ul>\n\n\n\n<p>Dal\u0161\u00edmi mo\u017enostmi l\u00e9\u010dby jsou intraven\u00f3zn\u00ed imunoglobulin (IVIG), plazmafer\u00e9za, rituximab a autologn\u00ed transplantace kmenov\u00fdch bun\u011bk, kter\u00e9 jsou v\u0161ak m\u00e9n\u011b \u010dast\u00e9.<\/p>\n\n\n\n<h2>Prom\u011b\u0148te sv\u00e1 data ve snadno pochopiteln\u00e9, dynamick\u00e9 p\u0159\u00edb\u011bhy<\/h2>\n\n\n\n<p>P\u0159i sd\u011blov\u00e1n\u00ed d\u016fle\u017eit\u00fdch informac\u00ed ve va\u0161\u00ed pr\u00e1ci je velmi d\u016fle\u017eit\u00e9 zajistit, aby poslucha\u010di zcela rozum\u011bli tomu, co \u0159\u00edk\u00e1te. V\u011bd\u011bli jste, \u017ee barevn\u00e9 vizualizace zlep\u0161uj\u00ed n\u00e1chylnost lid\u00ed \u010d\u00edst text o 80%? (Zdroj: Saurage Research) Vyu\u017e\u00edvejte <a href=\"https:\/\/mindthegraph.com\" target=\"_blank\" rel=\"noreferrer noopener\">Pozor na graf<\/a> a vyberte \u0161ablonu, kter\u00e1 nejl\u00e9pe vystihuje va\u0161i pr\u00e1ci!<\/p>\n\n\n\n<div style=\"height:18px\" aria-hidden=\"true\" class=\"wp-block-spacer\"><\/div>\n\n\n<div class=\"wp-block-image\">\n<figure class=\"aligncenter size-full\"><img decoding=\"async\" loading=\"lazy\" width=\"600\" height=\"338\" src=\"https:\/\/mindthegraph.com\/blog\/wp-content\/uploads\/2022\/10\/r3qiu0qenda-3.gif\" alt=\"\" class=\"wp-image-25130\"\/><\/figure><\/div>\n\n\n<div style=\"height:18px\" aria-hidden=\"true\" class=\"wp-block-spacer\"><\/div>\n\n\n\n<div class=\"is-layout-flex wp-block-buttons\">\n<div class=\"wp-block-button aligncenter\"><a class=\"wp-block-button__link has-background wp-element-button\" href=\"https:\/\/mindthegraph.com\/\" style=\"border-radius:50px;background-color:#dc1866\" target=\"_blank\" rel=\"noreferrer noopener\">Zve\u0159ejn\u00edme v\u00e1\u0161 v\u00fdzkum<\/a><\/div>\n<\/div>\n\n\n\n<div style=\"height:44px\" aria-hidden=\"true\" class=\"wp-block-spacer\"><\/div>\n\n\n\n<div style=\"height:25px\" aria-hidden=\"true\" class=\"wp-block-spacer\"><\/div>\n\n\n\n<p><\/p>","protected":false},"excerpt":{"rendered":"<p>V tomto \u010dl\u00e1nku se dozv\u00edte v\u0161e, co pot\u0159ebujete v\u011bd\u011bt o syndromu ztuhlosti, neobvykl\u00e9m autoimunitn\u00edm onemocn\u011bn\u00ed. <\/p>","protected":false},"author":28,"featured_media":25956,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":[],"categories":[959,28],"tags":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v19.9 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Stiff Person Syndrome: Symptoms, Causes, and Treatment<\/title>\n<meta name=\"description\" content=\"This article will teach you all you need to know about Stiff Person Syndrome, 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Jessica is an animal rights activist who enjoys reading and drinking strong coffee.","sameAs":["https:\/\/www.linkedin.com\/in\/jessica-abbadia-9b834a13b\/"],"url":"https:\/\/mindthegraph.com\/blog\/cs\/author\/jessica\/"}]}},"_links":{"self":[{"href":"https:\/\/mindthegraph.com\/blog\/cs\/wp-json\/wp\/v2\/posts\/25947"}],"collection":[{"href":"https:\/\/mindthegraph.com\/blog\/cs\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/mindthegraph.com\/blog\/cs\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/mindthegraph.com\/blog\/cs\/wp-json\/wp\/v2\/users\/28"}],"replies":[{"embeddable":true,"href":"https:\/\/mindthegraph.com\/blog\/cs\/wp-json\/wp\/v2\/comments?post=25947"}],"version-history":[{"count":4,"href":"https:\/\/mindthegraph.com\/blog\/cs\/wp-json\/wp\/v2\/posts\/25947\/revisions"}],"predecessor-version":[{"id":25963,"href":"https:\/\/mindthegraph.com\/blog\/cs\/wp-json\/wp\/v2\/posts\/25947\/revisions\/25963"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/mindthegraph.com\/blog\/cs\/wp-json\/wp\/v2\/media\/25956"}],"wp:attachment":[{"href":"https:\/\/mindthegraph.com\/blog\/cs\/wp-json\/wp\/v2\/media?parent=25947"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/mindthegraph.com\/blog\/cs\/wp-json\/wp\/v2\/categories?post=25947"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/mindthegraph.com\/blog\/cs\/wp-json\/wp\/v2\/tags?post=25947"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}